evrazkarЕвразийский Кардиологический ЖурналEurasian heart journal2225-16852305-0748Евразийская ассоциация кардиологов10.38109/2225-1685-2020-1-130-135evrazkar-5391Research ArticleОБЗОРREVIEWОСНОВНЫЕ АСПЕКТЫ СИНДРОМА БРУГАДАMAIN ASPECTS OF BRUGADA SYNDROMEhttps://orcid.org/0000-0003-4400-2561ДульченкоВ. С.DulchenkoV. S.

Дульченко Валентина Сергеевна, студентка

Dulchenko Valentina Segeevna, student

https://orcid.org/0000-0002-6260-7102ВасиленкоА. А.VasilenkoA. A.

Василенко Анна Анатольевна, студентка

Vasilenko Anna Anatolyevna, student

https://orcid.org/0000-0002-4097-6409МагомедоваА. Х.MagomedovaA. H.

Магомедова Алина Хасановна, студентка

Magomedova Alina Khasanovna, student

https://orcid.org/0000-0002-1250-8798ХидироваЛ. Д.KhidirovaL. D.

Хидирова Людмила Давыдовна, кандидат медицинских наук, доцент

630091, Новосибирск, ул. Залесского, 6, корп. 8.

тел. 8 (383) 275 00 52

Khidirova Lyudmila Davydovna, PhD, FSBEI of Higher Education

630091, Novosibirsk, Russia, st. Zalessky, 6, Bldg. 8

h_ludmila73@mail.ru«Новосибирский государственный медицинский университет» Минздрава РоссииРоссияNovosibirsk State Medical UniversityRussian Federation20203003202001130135Copyright © Дульченко В.С., Василенко А.А., Магомедова А.Х., Хидирова Л.Д., 20202020Дульченко В.С., Василенко А.А., Магомедова А.Х., Хидирова Л.Д.Dulchenko V.S., Vasilenko A.A., Magomedova A.H., Khidirova L.D.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.heartj.asia/jour/article/view/5391

На сегодняшний день накоплено достаточное количество данных о природе заболеваний, сопряженных с риском внезапной смерти. Показано, что многие из них генетически детерминированы, а это представляет особую опасность, так как под угрозой находится не только больной, у которого выявили заболевание, но и его дети и близкие родственники. Такие заболевания редко выявляются в обычной клинической практике, и больные умирают, как правило, не в специализированных стационарах, а дома или на улице, и врачу поликлиники или бригаде скорой помощи остается констатировать смерть.

Кардиологи, нередко, обращают внимание только на первые симптомы заболевания, прежде всего синкопе и приступы сердцебиения, но также нередко первым и последним проявлением заболевания становится внезапная смерть.

Современная клинической медицина выделяет ряд заболеваний и синдромов, тесно ассоциированных с высоким риском внезапной смерти в молодом возрасте. К ним относится и одно из наиболее «загадочных» заболеваний — синдром Бругада (CБ).

To date, there is a sufficient amount of data on the nature of diseases associated with the risk of sudden death. It is shown that many of them are genetically determined, and this is particularly dangerous, since not only the patient who has been diagnosed with the disease, but also his children and close relatives are at risk. Such diseases are rarely detected in normal clinical practice, and patients die, as a rule, not in specialized hospitals, but at home or on the street, and the doctor of the polyclinic or the ambulance crew remains to state the death. Cardiologists often pay attention only to the first symptoms of the disease, primarily syncope and palpitations, but also often the first and last manifestation of the disease is sudden death. Modern clinical medicine identifies a number of diseases and syndromes that are closely associated with a high risk of sudden death at a young age. These include one of the most «mysterious» diseases — Brugada syndrome (SB).

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The authors declare that there are no conflicts of interest present.